Follicular mucinosis is an uncommon inflammatory disorder that characteristically presents as follicular papules and/or indurated plaques. The face, neck, and. Pages Mucinosis folicular: nuevas entidades clínico-patológicas. Estudio clínico, histológico, inmunohistoquímico e inmunogenotípico de 23 pacientes*. Follicular Mucinosis in Childhood: A Case Report and Review of the Literature. Mucinosis folicular en la infancia: aportación de un caso y revisión de la.

Author: Maladal Yozshunos
Country: Brazil
Language: English (Spanish)
Genre: Video
Published (Last): 13 March 2018
Pages: 475
PDF File Size: 20.94 Mb
ePub File Size: 7.46 Mb
ISBN: 126-2-43652-620-4
Downloads: 36800
Price: Free* [*Free Regsitration Required]
Uploader: Goltisar

Follicular mucinosis FMu is a relatively rare dermatosis, belonging to the cutaneous mucinoses group, that is, a complex of morphological and various etiopathogenic clinical entities, whose common denominator is represented by localized or diffused deposits of mucin in the skin or hair follicles. Mucinosis folicular en la infancia: Pathophysiology Alopecia mucinosa is a disease process defined histopathologically by mucin deposition in hair follicles and sebaceous glands, which undergo epithelial reticular degeneration.

A clinical mucinoiss histologic variant of cutaneous T-cell lymphoma: Erythematous-brownish oval-shaped plaque, well-circumscribed and infiltrated, measuring approximately 2.

Mucinosis folicular mcinosis la infancia: Diagnosis, differential; Leprosy, tuberculoid; Mucinosis, follicular.

Sign Muconosis It’s Free! In Rabello’s description 8the objective aspect of FMu is that of “flat or raised plaques, pink or reddish-purple in color, at times squamous or keratotic, edematous or infiltrated, with or without pruritus; these plaques are covered by open porous pilosebaceos, small follicular papules and alopecic areas.

In most patients who exhibit both alopecia mucinosa and mycosis fungoides, these conditions appear to develop concomitantly; however, the concern exists that individuals exhibiting only alopecia mucinosa may also be at risk for subsequent development of lymphoma.


Options for Treatment Follicular Mycosis Fungoides: Author information Copyright and License information Disclaimer. The pathogenesis of follicular mucinosis remains fooicular, being in some cases associated with lymphoproliferative disorders. Alopecia mucinosa is a disease process defined histopathologically by mucin deposition in hair follicles and sebaceous glands, which undergo epithelial reticular degeneration.

February 14, ; Accepted: Services on Demand Journal. The abnormal deposits that occur in mucinoiss can be localised or widespread. Show more Show less. Other less common presentations have been already described, with acneiform, eczematous, cystic or nodular lesions.

Prognosis The prognosis of alopecia mucinosa depends on the specific clinical variant, as follows: How to cite this article: It was described for the first time by Pinkus et al.

The primary disorder of young persons consists of focal cutaneous lesions with limited progression. Approved by the Consultive Council and accepted for publication in March, 23 th of PFM is also considered to be an idiopathic, benign and transient form of the disease.

The accumulation of mucinous material in the damaged hair follicles and sebaceous glands creates an inflammatory condition and subsequent degenerative process. If you log out, you will be required to enter your username and password the next time you mucinosos.

All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License. There are no clinical criteria to distinguish primary cases from cases associated with mycosis fungoides MF ; however, most patients with limited involvement tend to have a benign folicu,ar.

Benign idiopathic versus mycosis fungoides-associated follicular mucinosis.


Alopecia Mucinosa: Background, Pathophysiology, Epidemiology

Received in May, 25 th of Rio Branco, 39 Subscribe to our Newsletter. However, as the alopecia is only clinically evident when found to be affecting cutaneous areas with the terminal hairs, the FMu designation seems to be more adequate. Besides Hansen’s disease, primary Muvinosis must be differentiated from persistent reaction to insect bite, lymphocytoma and lymphocytic infiltrate, among others.

Funding goes towards fooicular articles for DermNet, supporting researchers, and improving dermatological knowledge around the world. The malignant potential of alopecia mucinosa cannot be fully assessed because of the enigmatic nature of this and other cutaneous T-cell abnormalities.

Find articles by Danielle Cristine Westphal. Journal List An Bras Dermatol v. PFM in young people tends to involve the head and neck, with resolution after 2 to 24 months. It is believed that follicular keratinocytes are responsible for mucin production, as a response to the stimulus of cytokines released by perifollicular T lymphocytes. This mucinosiss be followed by formation of cystic spaces partially mucin covered. Folliculotropic T-cell lymphocytosis mucin-poor follicular mucinosis.

Alopecia Mucinosa

The primary form occurs in children and young adults. Follicular mucinosis FM is a rare dermatosis whose etiology is not fully understood, characterized by the accumulation of mucin in the follicular epithelium and sebaceous glands.

Br J Dermatol ; suppl